Nailfold capillaroscopic changes in Kindler syndrome
نویسندگان
چکیده
منابع مشابه
Nailfold capillaroscopic findings in primary Sjögren's syndrome: clinical and serological correlations.
OBJECTIVE To describe the capillaroscopic abnormalities observed in patients with primary Sjögren's Syndrome (pSS), associating them with clinical and serologic features, and comparing these findings to those observed in normal controls. METHODS Sixty-one consecutive patients with pSS were studied by clinical evaluation, serology, and nailfold capillary microscopy (NCM). Twenty-one normal con...
متن کاملKindler syndrome.
Kindler syndrome is a rare autosomal recessive disorder associated with skin fragility. It is characterized by blistering in infancy, photosensitivity and progressive poikiloderma. The syndrome involves the skin and mucous membrane with radiological changes. The genetic defect has been identified on the short arm of chromosome 20. This report describes an 18-year-old patient with classical feat...
متن کاملGastrointestinal Manifestation of Kindler Syndrome
1. Kindler T. congenital poikiloderma with traumatic bulla formation and progressive cutaneous atrophy. Br J Dermatol 1954; 66: 104-11. 2. Yazdanfar A, Hashemi B. Kindler syndrome: report of three cases in a family and a brief review. Int J Dermatol 2009; 48:145-52. 3. Penagos H, Jaen M, Sancho MT, Saborio MR, Fallas VG, Siegel DH, et al. Kindler syndrome in Native Americans from Panama: report...
متن کاملPrevalence of Raynaud Phenomenon and Nailfold Capillaroscopic Abnormalities in Fabry Disease
Fabry disease (FD) is a lysosomal disorder leading to progressive systemic involvement, including microvascular damage that leads to neurological and cardiovascular disorders. We hypothesize that the latter could be documented at an early stage by performing a microcirculation study with nailfold capillaroscopy and evaluation of Raynaud phenomenon.The objective was to measure the prevalence of ...
متن کاملNailfold Capillaroscopic Monitoring as Preventive Medicine in Subjects Exposed to Ionising Radiation
Capillaroscopy consists of in vivo observation of microvessels using special microscopes with a short focal length. Normally, when looking at the nail fold, where capillaroscopy is commonly used, the capillaries are arranged like hairpins, lined up in parallel or obliquely to the field of vision in three or four layers above the subpapillary venous network, approximately 20 loops per mm. Ionisi...
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ژورنال
عنوان ژورنال: Intractable & Rare Diseases Research
سال: 2015
ISSN: 2186-361X,2186-3644
DOI: 10.5582/irdr.2015.01038